Non-invasive ventilation is associated with long-term improvements in lung function and gas exchange in cystic fibrosis adults with hypercapnic respiratory failure

Wadsworth, LE; Belcher, J; Bright-Thomas, RJ

Abstract

Non-invasive ventilation (NIV) is an established treatment option for cystic fibrosis (CF) patients with type 2 respiratory failure but the benefits of this therapy remain unclear. This study examined the long-term outcomes and response to NIV in a large adult CF cohort.

• Journal Article Type: Article
• Acceptance Date: May 17, 2021
• Online Publication Date: Jun 16, 2021
• Publication Date: 2021-09
• Deposit Date: Jun 2, 2023
• Journal: Journal of Cystic Fibrosis
• Print ISSN: 1569-1993
• Publisher: Elsevier
• Peer Reviewed: Peer Reviewed
• Volume: 20
• Issue: 5
• Pages: e40-e45
• DOI: https://doi.org/10.1016/j.jcf.2021.05.011
• Keywords: Pulmonary and Respiratory Medicine; Pediatrics, Perinatology and Child Health
• Additional Information: This article is maintained by: Elsevier; Article Title: Non-invasive ventilation is associated with long-term improvements in lung function and gas exchange in cystic fibrosis adults with hypercapnic respiratory failure; Journal Title: Journal of Cystic Fibrosis; CrossRef DOI link to publisher maintained version: https://doi.org/10.1016/j.jcf.2021.05.011; Content Type: article; Copyright: © 2021 European Cystic Fibrosis Society. Published by Elsevier B.V. All rights reserved.