Intravascular leiomyomatosis: A case report and review of the literature

Simon, A.J.; Parry-Smith, W.R.; Redman, C.W.E.; Kodampur, M.; Todd, R.; Satur, C.; Morgan, R.

Abstract

Intravascular leiomyomatosis (IVL) is a rare condition in which histologically benign smooth muscle neoplasms arising from the intrauterine vessels infiltrate and invade systemic veins, including the inferior vena cava (IVC) (CitationCho et al. 2011). These tumours can further extend to the right heart and into the pulmonary arterial system, causing a pulmonary embolism (CitationFasih et al. 2008). This is called intracardiac leiomyomatosis and may result in the development of cardiac symptoms, a murmur, syncope and even death (CitationLou et al. 2011). To correctly diagnose IVL pre-operatively, comprehensive imaging using computerised tomography (CT) and magnetic resonance imaging (MRI), and possibly other modalities, need to be incorporated (CitationPan et al. 2013). Treatment is surgical, with excision of the primary uterine mass and often cardiotomy to remove any intracardiac lesion; though, unusually, we present a case without the need for cardiotomy, a staged approach or cardiothoracic surgery (CitationLam et al. 2003).

Citation

Simon, A., Parry-Smith, W., Redman, C., Kodampur, M., Todd, R., Satur, C., & Morgan, R. (2015). Intravascular leiomyomatosis: A case report and review of the literature. Journal of Obstetrics and Gynaecology, 35, 539-540. https://doi.org/10.3109/01443615.2014.978847

• Journal Article Type: Article
• Online Publication Date: Nov 19, 2014
• Publication Date: 2015
• Deposit Date: Jun 6, 2024
• Journal: Journal of Obstetrics and Gynaecology
• Print ISSN: 0144-3615
• Publisher: Taylor and Francis
• Peer Reviewed: Peer Reviewed
• Volume: 35
• Pages: 539-540
• DOI: https://doi.org/10.3109/01443615.2014.978847
• Public URL: https://keele-repository.worktribe.com/output/773645
• Publisher URL: https://www.tandfonline.com/doi/full/10.3109/01443615.2014.978847